Congenital cholesteatoma of mastoid origin – A multicenter case series

Ljiljana Čvorović; Dragoslava Djerić; Ljiljana Vlaški; Dragan Dankuc; Ivan Baljošević; Ljubomir Pavićević

doi:10.2298/1430

Ljiljana Čvorović Faculty of Medicine, University of Belgrade, Belgrade, Serbia; Department of Otorhonolaringology, Clinical Center “Zemun”, Belgrade, Serbia
Dragoslava Djerić Faculty of Medicine, University of Belgrade, Belgrade, Serbia; Institute of Otorhinolaryngology, Clinical Center Serbia, Belgrade, Serbia
Ljiljana Vlaški Faculty of Medicine, University of Novi Sad and Clinical Center of Vojvodina, Novi Sad, Serbia
Dragan Dankuc Faculty of Medicine, University of Novi Sad and Clinical Center of Vojvodina, Novi Sad, Serbia
Ivan Baljošević Department of Otorhinolaryngology, Mother and Child Health Institute, Belgrade, Serbia
Ljubomir Pavićević Clinic for Otorhinolaryngology, Military Medical Academy, Belgrade, Serbia

DOI: https://doi.org/10.2298/1430

Keywords: cholesteatoma, congenital abnormalities, diagnosis, differential, otologic surgical procedures, recurrence,

Abstract

Background/Aim. The mastoid is the rarest site for the onset of congenital cholesteatoma (CC). The symptoms are atypical and minimal. The aim of this multicenter retrospective descriptive study was to define this extremely rare condition and its clinical presentation, diagnosis and management. Methods. We analyzed data files for a 15-year period in 4 tertiary otology centers and discovered 6 patients with the diagnosis of CC of the mastoid. Results. The clinical presentation of CC varied from incidental findings in patient to patient with otogenic meningitis. The most common findings during surgical procedures were mastoid cortex erosion, sigmoid plate dehiscence, dural exposure and external canal wall destruction. Conclusion. CC of mastoid origin tends to occur in adult patients probably because of minimal symptoms and the delayed diagnosis. It can exist for years in a nonaggressive state and develop to giant sizes. In children it is almost incidentally diagnosed. Early imaging is necessary in order to prevent serious complication.

Author Biography

Ljiljana Čvorović, Faculty of Medicine, University of Belgrade, Belgrade, Serbia; Department of Otorhonolaringology, Clinical Center “Zemun”, Belgrade, Serbia

Specijalista otorinolaringolog, Šef odeljenja ORL i MFH, doktor medicinskih nauka, klinički asistent

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